Chronic Thromboembolic Pulmonary Hypertension

In addition to chronic anticoagulation therapy, each patient with chronic thromboembolic disease (CTEPH) should receive treatment assessment starting with evaluation for pulmonary endarterectomy (PEA), which is the guideline recommended treatment.

For technically inoperable cases, PH-targeted medical therapy is recommended (currently riociguat based on the CHEST studies), and balloon pulmonary angioplasty should be considered at a centre experienced with this challenging but potentially effective and complementary intervention.