Cystic Fibrosis Evidence-Based Nutrition Recommendations

Publication Date: February 1, 2020

Introduction

Introduction

Cystic fibrosis (CF) is a genetic disease in which affected individuals produce thick, sticky mucus in multiple organs, including the lungs and pancreas. The complexity of this disease requires an interdisciplinary, integrated approach to care. Nutrition care is central to this approach, since poor nutritional status in individuals with CF is associated with disease decline. Nutritional status is likely to be compromised in individuals with CF, because CF increases energy needs as well as nutrient malabsorption.

Screening and Referral

...eening and Referra...

...f Nutrition Screening, Less Than 2 Years...


...Method of Nutrition Screening, Less Than...


...requency of Nutrition Screening, 2-...


...f Nutrition Screening, 2-20 Years of Age Pediatr...


...y of Nutrition Screening, Adults In adults w...


...of Nutrition Screening, Adults Adults w...


Nutrition Assessment

...utrition Assess...

...requency of Nutrition Assessment In individu...


...trition Assessment Components In individual...


...TR Modulators in Nutrition Assessment...


...: Indirect Calorimetry In pediatric (≤20...


...g Energy Needs, Pediatrics In pediatr...


...: Estimating Energy Needs, Adults In adults...


...y X-Ray Absorptiometry (DEXA) In individua...


...Single-Site Anthropometric Measures and Nutriti...


...Skinfold Measures and Bioelectrica...


...Tolerance Testing (OGTT) For individuals w...


...Vitamins For all individuals with CF, rega...


CF: Lipid Profile For individuals with CF, i...


Nutrition Intervention

...trition Intervention

...Approach RDNs or international equivalents sh...


...me Equivalents (FTEs) It is reasonable for one F...


CF: Food and Supplement Intake For all indivi...


...erns For all individuals with CF, it...


...Meal and Snack Frequency For all individuals...


...Intake with CF-Related Diabetes For all ind...


...F: Food Intake with Overweight/Obesi...


...utrient Distribution For individuals with...


...e For individuals with CF, the RDN or internati...


...ant Feeding In infants diagnosed...


Nutrition Monitoring and Evaluation 

...itoring and Evaluation ...