Cystic Fibrosis Evidence-Based Nutrition Recommendations

Publication Date: February 1, 2020

Introduction

Introduction

Cystic fibrosis (CF) is a genetic disease in which affected individuals produce thick, sticky mucus in multiple organs, including the lungs and pancreas. The complexity of this disease requires an interdisciplinary, integrated approach to care. Nutrition care is central to this approach, since poor nutritional status in individuals with CF is associated with disease decline. Nutritional status is likely to be compromised in individuals with CF, because CF increases energy needs as well as nutrient malabsorption.

Screening and Referral

...ing and Referral...

CF: Frequency of Nutrition Screening,...


...trition Screening, Less Than 2 Years of Age...


...of Nutrition Screening, 2-20 Years o...


...Nutrition Screening, 2-20 Years of Age...


...quency of Nutrition Screening, Adul...


...Nutrition Screening, Adults Adul...


Nutrition Assessment

...trition Assessment

...requency of Nutrition Assessment In ind...


...trition Assessment Components In indivi...


...FTR Modulators in Nutrition Assessment For indi...


...rect Calorimetry In pediatric (≤2...


...ating Energy Needs, Pediatrics In p...


...ating Energy Needs, Adults In adults with C...


...Energy X-Ray Absorptiometry (DEXA) In individu...


...le-Site Anthropometric Measures and Nutrition Foc...


...f Skinfold Measures and Bioelectri...


CF: Oral Glucose Tolerance Testing (OGTT) For ind...


...t-Soluble Vitamins For all individuals with...


...Lipid Profile For individuals with CF, it is re...


Nutrition Intervention

...trition Interve...

... RDNs or international equivalents should...


...MNT Full-Time Equivalents (FTEs) I...


...nd Supplement Intake For all individuals...


...ary Patterns For all individuals with CF, it...


...al and Snack Frequency For all individuals wit...


...ke with CF-Related Diabetes For a...


...ntake with Overweight/Obesity For ind...


...onutrient Distribution For individuals with CF wh...


...take For individuals with CF, the RDN or...


...nt Feeding In infants diagnosed with...


Nutrition Monitoring and Evaluation 

...Monitoring and Evaluation ...