Cystic Fibrosis Evidence-Based Nutrition Recommendations

Publication Date: February 1, 2020

Introduction

Introduction

Cystic fibrosis (CF) is a genetic disease in which affected individuals produce thick, sticky mucus in multiple organs, including the lungs and pancreas. The complexity of this disease requires an interdisciplinary, integrated approach to care. Nutrition care is central to this approach, since poor nutritional status in individuals with CF is associated with disease decline. Nutritional status is likely to be compromised in individuals with CF, because CF increases energy needs as well as nutrient malabsorption.

Screening and Referral

...Screenin...

...cy of Nutrition Screening, Less Than 2 Years...


...f Nutrition Screening, Less Than 2 Years of Age...


CF: Frequency of Nutrition Screenin...


...Method of Nutrition Screening, 2-20 Years of...


CF: Frequency of Nutrition Screening, Ad...


...f Nutrition Screening, Adults Adults...


Nutrition Assessment

...Nutrition...

...uency of Nutrition Assessment In individual...


...tion Assessment Components In individua...


...ulators in Nutrition Assessment For indiv...


...orimetry In pediatric (≤20 years...


...mating Energy Needs, Pediatrics In pediatric i...


...stimating Energy Needs, Adults In adults w...


...Dual-Energy X-Ray Absorptiometry (DEXA) In in...


...ite Anthropometric Measures and Nutrition Focused...


...cy of Skinfold Measures and Bioele...


...ral Glucose Tolerance Testing (OGTT) F...


...Vitamins For all individuals with CF, regar...


...ipid Profile For individuals with CF,...


Nutrition Intervention

...Nutrition...

...T Approach RDNs or international equivale...


...F: MNT Full-Time Equivalents (FTEs) It is reas...


...Food and Supplement Intake For all i...


...ry Patterns For all individuals with CF,...


...and Snack Frequency For all individ...


...e with CF-Related Diabetes For all individuals w...


...Intake with Overweight/Obesity For individu...


...acronutrient Distribution For individuals with C...


...r Intake For individuals with CF, the...


...nt Feeding In infants diagnosed with CF, the RD...


Nutrition Monitoring and Evaluation 

...Nutrition Mo...