Cystic Fibrosis Evidence-Based Nutrition Recommendations

Publication Date: February 1, 2020

Introduction

Introduction

Cystic fibrosis (CF) is a genetic disease in which affected individuals produce thick, sticky mucus in multiple organs, including the lungs and pancreas. The complexity of this disease requires an interdisciplinary, integrated approach to care. Nutrition care is central to this approach, since poor nutritional status in individuals with CF is associated with disease decline. Nutritional status is likely to be compromised in individuals with CF, because CF increases energy needs as well as nutrient malabsorption.

Screening and Referral

...ning and Referral...

...Frequency of Nutrition Screening, Less Than 2 Y...


...trition Screening, Less Than 2 Years of Age...


...equency of Nutrition Screening, 2-20 Year...


...trition Screening, 2-20 Years of Age Pediat...


...equency of Nutrition Screening, Adults In adult...


...Method of Nutrition Screening, Adults Ad...


Nutrition Assessment

...ition Assessment

...equency of Nutrition Assessment In ind...


...Nutrition Assessment Components In i...


CF: CFTR Modulators in Nutrition Assess...


CF: Indirect Calorimetry In pediatric (≤20 year...


...Estimating Energy Needs, Pediatrics In pe...


...F: Estimating Energy Needs, Adults...


...nergy X-Ray Absorptiometry (DEXA) In individu...


...ngle-Site Anthropometric Measures and Nutriti...


...Skinfold Measures and Bioelectrical Impedance Ana...


...ral Glucose Tolerance Testing (OGTT) F...


...: Fat-Soluble Vitamins For all indivi...


...e For individuals with CF, it is reasonable...


Nutrition Intervention

...utrition Intervention...

...F: MNT Approach RDNs or international equivalent...


...MNT Full-Time Equivalents (FTEs) It is rea...


...upplement Intake For all individuals with CF, it...


...F: Dietary Patterns For all individual...


...and Snack Frequency For all indiv...


...ke with CF-Related Diabetes For all individu...


...e with Overweight/Obesity For individual...


...F: Macronutrient Distribution For...


...Fiber Intake For individuals with CF, the RD...


...Infant Feeding In infants diagnosed...


Nutrition Monitoring and Evaluation 

...on Monitoring and Evaluation ...