Cystic Fibrosis Evidence-Based Nutrition Recommendations

Publication Date: February 1, 2020

Introduction

Introduction

Cystic fibrosis (CF) is a genetic disease in which affected individuals produce thick, sticky mucus in multiple organs, including the lungs and pancreas. The complexity of this disease requires an interdisciplinary, integrated approach to care. Nutrition care is central to this approach, since poor nutritional status in individuals with CF is associated with disease decline. Nutritional status is likely to be compromised in individuals with CF, because CF increases energy needs as well as nutrient malabsorption.

Screening and Referral

...Screen...

...cy of Nutrition Screening, Less Than 2 Year...


...Nutrition Screening, Less Than 2 Ye...


...Nutrition Screening, 2-20 Years of Age F...


...of Nutrition Screening, 2-20 Years of Age¬...


...F: Frequency of Nutrition Screening, Adul...


CF: Method of Nutrition Screening, Adults Adults...


Nutrition Assessment

...Nutrition Assessm...

...ency of Nutrition Assessment In individua...


...ion Assessment Components In individuals with CF...


...: CFTR Modulators in Nutrition Assessmen...


...t Calorimetry¬†In pediatric (‚ȧ20 years of age)...


...g Energy Needs, Pediatrics In pediat...


...ng Energy Needs, Adults In adults with...


...X-Ray Absorptiometry (DEXA) In individuals with...


...Anthropometric Measures and Nutrition Focused Ph...


...Skinfold Measures and Bioelectrical Impedance...


...ucose Tolerance Testing (OGTT) For...


...ble Vitamins For all individuals wi...


...id Profile For individuals with CF, it is reasona...


Nutrition Intervention

...N...

...pproach RDNs or international equivalents s...


...ull-Time Equivalents (FTEs) It is reasonable...


...Supplement Intake For all individuals with CF, i...


...ietary Patterns For all individuals wi...


...and Snack Frequency For all individuals w...


...ke with CF-Related Diabetes For al...


...with Overweight/Obesity For individuals...


...acronutrient Distribution For individuals with CF...


...ake For individuals with CF, the RDN...


...Infant Feeding In infants diagnosed with CF...


Nutrition Monitoring and Evaluation 

...Nutrition Moni...