Title
Idiopathic Pulmonary Fibrosis and Progressive Pulmonary Fibrosis in Adults
Authoring Organizations
Publication Month/Year
April 29, 2022
Last Updated Month/Year
February 12, 2024
Supplemental Implementation Tools
Document Type
Guideline
Country of Publication
US
Document Objectives
This American Thoracic Society, European Respiratory Society, Japanese Respiratory Society, and Asociación Latinoamericana de Tórax guideline updates prior idiopathic pulmonary fibrosis (IPF) guidelines and addresses the progression of pulmonary fibrosis in patients with interstitial lung diseases (ILDs) other than IPF.
Target Patient Population
Adults with pulmonary fibrosis
Target Provider Population
Pulmonologists, critical care specialists and other allied providers caring for patients with pulmonary fibrosis
Inclusion Criteria
Male, Female, Adult, Older adult
Health Care Settings
Ambulatory, Hospital, Laboratory services, Outpatient
Intended Users
Nurse, nurse practitioner, physician, physician assistant
Scope
Diagnosis, Assessment and screening, Treatment, Management, Prevention
Diseases/Conditions (MeSH)
D054990 - Idiopathic Pulmonary Fibrosis, D017563 - Lung Diseases, Interstitial, D011658 - Pulmonary Fibrosis
Keywords
interstitial lung disease, Idiopathic pulmonary fibrosis (IPF), IPF, ILD, PPF, Progressive Pulmonary Fibrosis
Source Citation
Raghu G, Remy-Jardin M, Richeldi L, Thomson CC, Inoue Y, Johkoh T, Kreuter M, Lynch DA, Maher TM, Martinez FJ, Molina-Molina M, Myers JL, Nicholson AG, Ryerson CJ, Strek ME, Troy LK, Wijsenbeek M, Mammen MJ, Hossain T, Bissell BD, Herman DD, Hon SM, Kheir F, Khor YH, Macrea M, Antoniou KM, Bouros D, Buendia-Roldan I, Caro F, Crestani B, Ho L, Morisset J, Olson AL, Podolanczuk A, Poletti V, Selman M, Ewing T, Jones S, Knight SL, Ghazipura M, Wilson KC. Idiopathic Pulmonary Fibrosis (an Update) and Progressive Pulmonary Fibrosis in Adults: An Official ATS/ERS/JRS/ALAT Clinical Practice Guideline. Am J Respir Crit Care Med. 2022 May 1;205(9):e18-e47. doi: 10.1164/rccm.202202-0399ST. PMID: 35486072.
Supplemental Methodology Resources
Data Supplement, Systematic Review Document, Systematic Review Document, Systematic Review Document, Systematic Review Document, Systematic Review Document