Idiopathic Pulmonary Fibrosis and Progressive Pulmonary Fibrosis in Adults
Introduction
Introduction
- Progress in the diagnosis and treatment of idiopathic pulmonary fibrosis (IPF) and other interstitial lung diseases (ILDs) manifesting progressive pulmonary fibrosis (PPF) has generated the need for updating guidelines.
- These recommendations are not mandates because they cannot account for all unique clinical circumstances and should be revisited as new evidence is published.
Recommendations
Recommendatio...
...e on the Diagnosis and Treatment of IPF...
...gest transbronchial lung cryobiopsy (TBLC) be...
...no recommendation for or against the a...
...uggest not treating patients with IPF with a...
...suggest not referring patients with IPF for ant...
...art II. Diagnosis and Treatment of PPF Other Than...
...fenidone...
...mmend further research into the efficacy, effec...
Nintedani...
...ggest nintedanib for the treatment of PPF...
...research into the efficacy, effective...
Tables
...bles
...gh-resolution Computed Tomography...
...2. Definition of PPFHaving trouble viewing t...
...ble 3. Selected Fibrotic Lung Diseases That C...
Figures
...gures...
...IPF Diagnosis Based Upon HRCT and Biopsy Patte...
...Diagnostic Algorithm for IPFa Patients...
...atic Pathway for Clinical Management of Patients W...
...ILD Manifesting PPFa The committee acknow...
...ion Bronchiectasis/bronchiolectasisA...
...igure 6. HoneycombingAxial, sagittal, an...
...ure 7. Paraseptal EmphysemaAxial and coronal...
...gure 8. Airspace Enlargement With Fibrosis (A...
Figure 9. Spectrum of CT Appearances in UIP Patter...
...attern Due to Connective Disease CTD-UIP Pattern...
...gure 11. Combined PPFE and UIP PatternsCorona...
...2. Three of the Four High-resolution C...
...gure 13. PPF in a Patient With IPF (Pr...
...re 14. PPF Due to NSIPA) CT in a 45...