Idiopathic Pulmonary Fibrosis and Progressive Pulmonary Fibrosis in Adults
Introduction
Introduction
- Progress in the diagnosis and treatment of idiopathic pulmonary fibrosis (IPF) and other interstitial lung diseases (ILDs) manifesting progressive pulmonary fibrosis (PPF) has generated the need for updating guidelines.
- These recommendations are not mandates because they cannot account for all unique clinical circumstances and should be revisited as new evidence is published.
Recommendations
...Recommendations...
...Part...
...transbronchial lung cryobiopsy (TBLC) be regarded...
We make no recommendation for or a...
...not treating patients with IPF with antacid me...
...e suggest not referring patients with IPF for a...
...Part II. Diagnos...
...P...
...recommend further research into the...
...est nintedanib for the treatment of PPF in pati...
...d research into the efficacy, effectiveness, and...
Tables
...Tabl...
...1. High-resolution Computed Tomograp...
...2. Definition of PPFIn a patient with ILD of...
...ected Fibrotic Lung Diseases That Can M...
Figures
...1. IPF Diagnosis Based Upon HRCT and Biopsy Pa...
...agnostic Algorithm for IPF a Patients...
...Schematic Pathway for Clinical Management...
...ILD Manifesting PPF a The committee ack...
...ction Bronchiectasis/bronchiolectasis...
...combing Axial, sagittal, and coronal CT im...
...ure 7. Paraseptal Emphysema Axial and coronal...
...space Enlargement With Fibrosis (AEF), Also Ca...
...ctrum of CT Appearances in UIP Pattern Due...
...Pattern Due to Connective Disease CTD-UIP Pattern...
...Combined PPFE and UIP Patterns Coronal CT image sh...
...Three of the Four High-resolution CT...
...igure 13. PPF in a Patient With IPF...
...ue to NSIP A) CT in a 45 year old...