Idiopathic Pulmonary Fibrosis and Progressive Pulmonary Fibrosis in Adults
Introduction
Introduction
- Progress in the diagnosis and treatment of idiopathic pulmonary fibrosis (IPF) and other interstitial lung diseases (ILDs) manifesting progressive pulmonary fibrosis (PPF) has generated the need for updating guidelines.
- These recommendations are not mandates because they cannot account for all unique clinical circumstances and should be revisited as new evidence is published.
Recommendations
...Recommenda...
...Part I. Upda...
...uggest transbronchial lung cryobiop...
...no recommendation for or against the addit...
...reating patients with IPF with ant...
...suggest not referring patients with IPF...
...Part II. Diagnosis a...
...Pirfenidon...
...ther research into the efficacy, eff...
...Nintedanib...
...suggest nintedanib for the treatm...
...end research into the efficacy, effectivenes...
Tables
...Tables...
...1. High-resolution Computed Tomograp...
...efinition of PPFHaving trouble viewing...
...Selected Fibrotic Lung Diseases That Can...
Figures
...Figures...
...iagnosis Based Upon HRCT and Biops...
...ostic Algorithm for IPFa Patients with a ra...
...matic Pathway for Clinical Management of Patients...
.... ILD Manifesting PPFa The committ...
...re 5. Traction Bronchiectasis/bronchiol...
Figure 6. HoneycombingAxial, sagitta...
...septal EmphysemaAxial and coronal C...
...space Enlargement With Fibrosis (AEF), Also...
Figure 9. Spectrum of CT Appearances in UIP Pa...
.... UIP Pattern Due to Connective Di...
...Combined PPFE and UIP PatternsCoronal CT image sh...
...ure 12. Three of the Four High-resolution...
...13. PPF in a Patient With IPF (Probable...
...14. PPF Due to NSIPA) CT in a 45 year old wo...