Hereditary Angioedema, Acquired C1 Inhibitor Deficiency, and Angiotensin-Converting Enzyme Inhibitor–Associated Angioedema

Authoring Organizations

Publication Month/Year

June 1, 2013

Last Updated Month/Year

August 22, 2023

Document Type


External Publication Status


Country of Publication


Inclusion Criteria

Female, Male, Adolescent, Adult, Child, Infant, Older adult

Health Care Settings

Ambulatory, Outpatient

Intended Users

Nurse, nurse practitioner, physician, physician assistant


Diagnosis, Prevention, Management, Treatment

Diseases/Conditions (MeSH)

D054179 - Angioedemas, Hereditary, D056828 - Hereditary Angioedema Type III, D056829 - Hereditary Angioedema Types I and II


angioedema, hereditary angioedema, HAE, acquired C1 inhibitor deficiency, C1 Inhibitor Deficiency, C1INH deficiency

Source Citation

Busse PJ, Christiansen SC, Riedl MA, Banerji A, Bernstein JA, Castaldo AJ, Craig T, Davis-Lorton M, Frank MM, Li HH, Lumry WR, Zuraw BL. US HAEA Medical Advisory Board 2020 Guidelines for the Management of Hereditary Angioedema. J Allergy Clin Immunol Pract. 2021 Jan;9(1):132-150.e3. doi: 10.1016/j.jaip.2020.08.046. Epub 2020 Sep 6. PMID: 32898710.