Hereditary Angioedema
Key Points
Key Points
Diagnosis
...agnosis...
...1. Complement Levels in the Diagnosis of H...
...gure 1. Recurrent Angioedema – Diagnosti...
Prevention
...evention...
...ment with replacement plasma-derived C1INH...
...agents for treatment of patients w...
...low to moderate doses of anabolic and...
...reatment with antifibrinolytic agents p...
...phylaxis can be achieved with fresh...
...need for long-term HAE prophylaxis...
...dose and effectiveness of long-term proph...
...ategies such as avoidance of ACE-Is, avoidance...
...of action of 17α-alkylated androg...
Pregnancy might be associated with an...
Treatment
...eatment
...h HAE-specific agent. Evidence from double-...
...t of HAE attacks may involve symptomatic treatment...
...plasma is often effective in abrogatin...
Neither anabolic androgens nor antifibrinolyt...
...ephrine, corticosteroids and antihistamines are NO...
Figure 2. HAE Treatment Algorithm
...HAE-Specific AgentsHaving trouble viewing table...
...Commonly Used for Long-term HAE Prophylaxis...
Special Cases
...ial Cases...
...th normal C1INH level...
...amilial recurrent angioedema characte...
...eds with HAE with normal C1INH leve...
...normal C1INH levels may be caused by...
Drugs developed for patients with HAE with reduce...
...red C1INH Deficiency...
...l characteristics of angioedema episodes i...
...uired C1INH deficiency involves demonstration...
...deficiency results from enhanced...
...d C1INH deficiency might be associated...
...of acquired C1INH deficiency is similar to...
...I–Associated Angioed...
...associated with angioedema in approx...
The management of ACE-I (or ARB)–asso...
...he angioedema associated with ACE-Is is likely...
...recurrent angioedema exists in patients wh...