Hereditary Angioedema
Key Points
Key Points
Diagnosis
...agnosis...
...omplement Levels in the Diagnosis of HAEHaving t...
Figure 1. Recurrent Angioedema â€...
Prevention
Prevention
...nt with replacement plasma-derived C1IN...
...gents for treatment of patients with C1INH d...
...t with low to moderate doses of anab...
...antifibrinolytic agents provides somewhat effect...
...ylaxis can be achieved with fresh frozen pla...
...r long-term HAE prophylaxis must be indiv...
...dose and effectiveness of long-term prophyla...
...ategies such as avoidance of ACE-Is,...
Mechanisms of action of 17α-alkylated androg...
...t be associated with an increase i...
Treatment
...atment...
...l patients with HAE-specific agent. Eviden...
...E attacks may involve symptomatic treatment...
...h frozen plasma is often effective in a...
...ther anabolic androgens nor antifibrinolytic drug...
..., corticosteroids and antihistamines are NOT...
Figure 2. HAE Treatment Algorithm
Table 2. HAE-Specific AgentsHaving tro...
...rugs Commonly Used for Long-term H...
Special Cases
...ial Cases...
...normal C1INH level
Familial recurrent angioedema characterized by...
...e kindreds with HAE with normal C1INH level...
...AE with normal C1INH levels may be caused by incr...
...d for patients with HAE with reduced C1INH func...
...red C1INH Deficiency...
...characteristics of angioedema episodes...
...gnosis of acquired C1INH deficiency involves dem...
...uired C1INH deficiency results from enhanc...
Acquired C1INH deficiency might be associated wi...
...ent of acquired C1INH deficiency is similar t...
...ssociated Angioedema...
...associated with angioedema in approxima...
...ent of ACE-I (or ARB)–associated angioedema...
...a associated with ACE-Is is likely due to i...
...f recurrent angioedema exists in patients who...